1～100

1. 丹羽公一郎，中澤誠，赤木禎治，他編著．成人の先天性心疾患診療ブック．メジカルビュー社 2008.

2. Shiina Y, Toyoda T, Kawasoe Y, et al. Prevalence of adultpatients with congenital heart disease in Japan. Int J Cardiol 2011; 146: 13-16.

3. 丹羽公一郎，立野滋，建部俊介，他．成人期先天性心疾患患者の社会的自立と問題点．J Cardiol 2002；39：259-266.

4. Warnes CA, Williams RG, Bashore TM, et al. ACC/AHA 2008 Guidelines for the Management of Adults With Congenital Heart Disease. A Report of the

American College of Cardiology/American Heart Association Task Force on Practice Guidelines (Writing Committee to Develop Guidelines on the

Management of Adults With Congenital Heart Disease): Developed in Collaboration With the American Society of Echocardiography, Heart Rhythm

Society, International Society for Adult Congenital Heart Disease, Society for Cardiovascular Angiography and Interventions, and Society of Thoracic

Surgeons Circulation 2008; 118: e714-e833.

5. Silversides CK, Marelli A, Beauchesne L, et al. Canadian Cardiovascular Society 2009 Consensus Conference on the management of adults with

congenital heart disease. Can J Cardiol 2010; 26: e70-117.

6. Baumgartner H, Bonhoeffer P, De Groot NMS, et al. ESC Guidelines for the management of grown-up congenital heart disease (new version 2010): The

Task Force on the Management of Grown-up Congenital Heart Disease of the European Society of Cardiology (ESC). Eur Heart J 2010; 31: 2915-2957.

7. Perloff JK, Child JS, Aboulhosn J (eds). Congenital Heart Disease in Adults (3rd ed). Saunders Elsevier 2008.

8. Gatzoulis MA, Webb GD, Daubeney PEF (eds). Diagnosis and Management of Adult Congenital Heart Disease. Churchill Livingstone 2003.

9. 循環器病の診断と治療に関するガイドライン．成人先天性心疾患診療ガイドライン．Jpn Circ J 2000；64，Suppl．Ⅳ： 1167-1204.

10. 循環器病の診断と治療に関するガイドライン．成人先天性心疾患診療ガイドライン（2006年改訂版）．

http://www.j-circ.or.jp/guideline/pdf/JCS2006_kurosawa_h.pdf（2010 年5月閲覧）．

11. 循環器病の診断と治療に関するガイドライン．先天性心疾患術後遠隔期の管理・侵襲的治療に関するガイドライン．Circ J 2007；71，Suppl, Ⅳ：1115-1189.

12. 循環器病の診断と治療に関するガイドライン．心疾患患者の妊娠・出産の適応，管理に関するガイドライン（2010年改訂版）．

http://www.j-circ.or.jp/guideline/pdf/JCS2010niwa.h.pdf（2010年5月閲覧）．

13. 循環器病の診断と治療に関するガイドライン．感染性心内膜炎の予防と治療に関するガイドライン（2008年改訂版）．

http://www.j-irc.or.jp/guideline/pdf/JCS2008_miyatake_h.pdf（2010年5月閲覧）.

14. 丹羽公一郎，中沢誠編著．新目でみる循環器病シリーズ14　成人先天性心疾患．メジカルビュー社 2005.

15. 丹羽公一郎編著．先天性心疾患の方のための妊娠・出産ガイドブック．中央法規出版 2006.

16. 丹羽公一郎，立野滋，豊田智彦，他編著．画像でみる成人先天性心疾患．メジカルビュー社 2010.

17. Khairy P, Hosn JA, Broberg C, et al. Multicenter research in adult congenital heart disease. Int J Cardiol 2008; 129: 155-159.

18. 丹羽公一郎．成人期の先天性心疾患の問題点．成人の先天性心疾患診療ブック（丹羽公一郎，中澤誠，赤木禎治，他編著）．メジカルビュー社 2008：31-33.

19. Terai M, Niwa K, Nakazawa M, et al. Mortality from congenital cardiovascular malformations in Japan, 1968 through 1997. Circ J 2002; 66: 484-488.

20. Perloff JK, Warnes CA. Congneital heart disease in adults: a new cardiovascular specialty. Circulation 2001; 84: 1881-1890.

21. Webb GD, Williams RG. 32nd Bethesda Conference:“ Care of the adult with congenital heart disease”. J Am Coll Cardiol 2001; 37: 1161-1198.

22. Marelli AJ, Mackie AS, Ionescu-Ittu R, et al. Congenital heart disease in the general population: changing prevalence and age distribution Circulation

2007; 115: 163-172.

23. Wacker A, Kaemmerer H, Hollweck R, et al. Outcome of operated and unoperated adults with congenital heart disease lost to follow-up for more than 5

years. Am J Cardiol 2005; 95: 776-779.

24. Warnes C, Liberthson R, Danielson GK, et al. Task force 1: the changing profile of congenital heart disease in adult life. J Am Coll Cardiol 2001; 37:

1170-1175.

25. Niwa K, Perloff JK, Webb GD, et al. Survey of specialized tertiary care facilities for adults with congenital heart disease. Int J Cardiol 2004; 96: 211-216.

26. Gatzoulis MA, Webb GD. Adults with congneital heart disease: A growing population. Diagnosis and Management of Adult Congneital Heart Disease

(Gatzoulis MA, Webb GD, Daubeney PEF. eds). Churchill Livingstone 2003: 3-6.

27. Hoffman JIE. Congenital heart disease: incidence and inheritance. Pediatr Clin North Am 1990; 37: 25-43.

28. Moller JH, Taubert KA, Allan HD, et al. Cardiovascular health and disease in children: current status. Circulation 1994; 89: 923-942.

29. Niwa K, Tateno S. Kawasaki’s disease. Diagnosis and Management of Adult Congenital Heart Disease. (Gatzoulis MA, Webb GD, Daubeney PEF.

eds). Churchill Livingstone 2003: 433-439.

30. Wren C, O’Sullivan JJ. Future demand for follow-up of adult survivors of congenital heart disease. Heart 2001; 85: 438-443.

31. Monro J. The changing state of surgery for adult congenital heart disease. Heart 2004; 91: 139-140.

32. 中澤誠，瀬口正史，高尾篤良．わが国における新生児心疾患の発生機序．（厚生省心身障害研究，心疾患研究班研究報告より）日小循誌 1986；90：2578-2587.

33. 日本小児循環器学会疫学委員会（松岡瑠美子ら）．先天性心血管疾患の疫学調査─1990年4月～1999年7月，2654家系の報告─　日小循誌 2003；19：606-

621.

34. Perloff JK, Warnes CA. Challenges posed by adults with repaired congenital heart disease. Circulation 2001; 103: 2637-2643.

35. Warnes CA.The adult with congenital heart disease: born to be bad? J Am Coll Cardiol 2005; 46: 1-8.

36. 藤田修平，高橋一浩，竹内大二，他．成人先天性心疾患患者の緊急入院について．日本心臓病学会誌 2009：3： 118-123.

37. Walsh EP, Cecchin F. Arrhythmias in adult patients with congenital heart disease. Circulation 2007; 115: 534-545.

38. Khairy P. EP challenges in adult congenital heart disease. Heart Rhythm 2008; 5: 1464-1472.

39. Dearani JA, Mavroudis C, Quintessenza J, et al. Surgical advances in the treatment of adults with congenital heart disease. Curr Opin Pediatr 2009; 21:

565-572.

40. Dietl CA, Cazzaniga ME, Dubner SJ, et al. Life-threatening arrhythmias and RV dysfunction after surgical repair of tetralogy of Fallot. Comparison

between transventricular and transatrial approaches. Circulation 1994; 90 (5 Pt 2): II7-12.

41. Rhodes LA, Wernovsky G, Keane JF, et al. Arrhythmias and intracardiac conduction after the arterial switch operation. J Thorac Cardiovasc Surg

1995;109: 303-310.

42. Hayashi G, Kurosaki K, Echigo S, et al. Prevalence of arrhythmias and their risk factors mid- and long-term after the arterial switch operation. Pediatr

Cardiol 2006; 27: 689-694.

43. d’Udekem Y, Iyengar AJ, Cochrane AD, et al. The Fontan procedure: contemporary techniques have improved longterm outcomes. Circulation 2007;

116 (11 Suppl): I157-164.

44. Hakacova N, Lakomy M, Kovacikova L. Arrhythmias after Fontan operation: comparison of lateral tunnel and extracardiac conduit. J Electrocardiol 2008;

41: 173-177.

45. Brown JW, Ruzmetov M, Deschner BW, et al. Lateral tunnel Fontan in the current era: is it still a good option? Ann Thorac Surg 2010; 89: 556-562.

46. Therrien J, Siu SC, Harris L, et al. Impact of pulmonary valve replacement on arrhythmia propensity late after repair of tetralogy of Fallot. Circulation

2001; 103: 2489-2494.

47. Harrild DM, Berul CI, Cecchin F, et al. Pulmonary valve replacement in tetralogy of Fallot: impact on survival and ventricular tachycardia. Circulation

2009; 119: 445-451.

48. Triedman JK, Alexander ME, Berul CI , et al .Electroanatomic mapping of entrained and exit zones in patients with repaired congenital heart disease

and intra-atrial reentrant tachycardia. Circulation 2001; 103: 2060-2065.

49. Nakagawa H, Shah N, Matsudaira K, et al. Characterization of reentrant circuit in macroreentrant right atrial tachycardia after surgical repair of

congenital heart disease: isolated channels between scars allow “focal” ablation. Circulation 2001; 103: 699-709.

50. Abrams DJ, Earley MJ, Sporton SC, et al. Comparison of noncontact and electroanatomic mapping to identify scar and arrhythmia late after the Fontan

procedure. Circulation 2007; 115: 1738-1746.

51. Zeppenfeld K, Schalij MJ, Bartelings MM, et al. Catheter ablation of ventricular tachycardia after repair of congenital heart disease: electroanatomic

identification of the critical right ventricular isthmus. Circulation 2007; 116: 2241-2252.

52. Khairy P, Harris L, Landzberg MJ, et al. Implantable cardioverter-defibrillators in tetralogy of Fallot. Circulation 2008; 117: 363-370.

53. Tsao S, Deal BJ, Backer CL, et al. Device management of arrhythmias after Fontan conversion. J Thorac Cardiovasc Surg 2009; 138: 937-940.

54. McLeod CJ, Kapa S, Asirvatham SJ. Implantable cardioverter-defibrillator therapy in congenital heart disease. Expert Rev Med Devices 2010; 7: 1-3.

55. Gilljam T, Mc Rindle BW, Smallhorn JE, et al. Outcomes of left atrial isomerism over a 28-year period at a single institution. J Am Coll Cardiol 2000; 36:

908-916.

56. Graham TP, Bernard YD, Mellen BG, et al. Long-term outcome in congenitally corrected transposition of the great arteries: a multi-institutional study. J

Am Coll Cardiol 2000; 36: 255-261.

57. Flinn CJ, Wolff GS, Dick M 2nd, et al. Cardiac rhythm after the Mustard operation for complete transposition of the great arteries. N Engl J Med 1984;

310: 1635-1638.

58. Manning PB, Mayer JE Jr, Wernovsky G, et al. Staged operation to Fontan increases the incidence of sinoatrial node dysfunction. J Thorac Cardiovasc

Surg 1996; 111: 833-839.

59. Wong T, Davlouros PA, Li W, et al. Mechano-electrical interaction late after Fontan operation: relation between P-wave duration and dispersion, right

atrial size, and atrial arrhythmias. Circulation 2004; 109: 2319-2325.

60. Epstein AE, DiMarco JP, Ellenbogen KA, et al. ACC/AHA/HRS 2008 Guidelines for Device-Based Therapy of Cardiac Rhythm Abnormalities: a report

of the American College of Cardiology/American Heart Association Task Force on Practice Guidelines (Writing Committee to Revise the ACC/

AHA/NASPE 2002 Guideline Update for Implantation of Cardiac Pacemakers and Antiarrhythmia Devices): developed in collaboration with the American

Association for Thoracic Surgery and Society of Thoracic Surgeons. Circulation 2008; 117: e350-408.

61. Soufflet V, Van de Bruaene A, Troost E, et al. Behavior of unrepaired perimembranous ventricular septal defect in young adults. Am J Cardiol 2010; 105:

404-407.

62. Roos-Hesselink J, Perlroth MG, McGhie J, et al. Atrial arrhythmias in adults after repair of tetralogy of Fallot. Correlations with clinical, exercise, and

echocardiographic findings. Circulation 1995; 91: 2214-2219

63. Gatzoulis MA, Balaji S, Webber SA, et al. Risk factors for arrhythmia and sudden cardiac death late after repair of tetralogy of Fallot: a multicentre

study. Lancet 2000; 356: 975-981.

64. Murphy JG, Gersh BJ, Mair DD, et al. Long-term outcome in patients undergoing surgical repair of tetralogy of Fallot.N Engl J Med 1993; 329: 593-599.

65. Ghai A, Harris L, Harrison DA, et al. Outcomes of late atrial tachyarrhythmias in adults after the Fontan operation.J Am Coll Cardiol 2001; 37: 585-592.

66. Takahashi K, Ushinohama H, Nakazawa M. Late atrial tachyarrhythmia and survival in 740 patients after Fontan operation: A Japanese multicenter

study. Circulation 2004; 110 (17 suppl III): III-651.

67. Puley G, Siu S, Connelly M, et al. Arrhythmia and survival in patients >18 years of age after the Mustard procedure for complete transposition of the

great arteries. Am J Cardiol 1999; 83: 1080-1084.

68. Feltes TF, Friedman RA. Transesophageal echocardiographic detection of atrial thrombi in patients with nonfibrillation atrial tachyarrhythmias and

congenital heart disease. J Am Coll Cardiol 1994; 24: 1365-1370.

69. 循環器病の診断と治療に関するガイドライン．慢性心不全治療ガイドライン（2010年改訂版）．http://www.j-circ.or.jp/guideline/pdf/JCS2010_matsuzaki_h.pdf

（2010 年5 月閲覧）．

70. Sietsema KE. Cyanotic congenital heart disease: dynamics of oxygen uptake and ventilation during exercise. J Am Coll Cardiol 1991; 18: 322-323.

71. Sietsema KE, Cooper DM, Perloff JK, et al. Control of ventilation during exercise in patients with central venous-tosystemic arterial shunts. J Appl

Physiol 1988; 64: 234-242.

72. Sietsema KE, Cooper DM, Perloff JK, et al. Dynamics of oxygen uptake during exercise in adults with cyanotic congenital heart disease. Circulation

1986; 73: 1137-1144.

73. Bolger AP, Coats AJ, Gatzoulis MA. Congenital heart disease: the original heart failure syndrome. Eur Heart J 2003; 24: 970-976.

74. Warnes CA, Somerville J. Tricuspid atresia in adolescents and adults: current state and late complications. Br Heart J 1986; 56: 535-543.

75. Remme WJ, Swedberg K. The task force for the diagnosis and treatment of chronic heart failure, European Society of Cardiology. Guidelines for the

diagnosis and treatment of chronic heart failure. Eur Heart J 2001; 22: 1527-1560.

76. Koch A, Zink S, Singer H. B-type natriuretic peptide in paediatric patients with congenital heart disease. Eur Heart J 2006; 27: 861-866.

77. Tulevski II, Groenink M, van der Wall EE, et al. Increased brain and atrial natriuretic peptides in patients with chronic right ventricular pressure overload:

correlation between plasma neurohormones and right ventricular dysfunction. Heart 2001; 86: 27-30.

78. Kikuchi K, Nishioka K, Ueda T, et al. Relationship between plasma atrial natriuretic polypeptide concentration and hemodynamic measurements in

children with congenital heart diseases. J Pediatr 1987; 111: 335-342.

79. Norozi K, Buchhorn R, Kaiser C, et al. Plasma N-terminal pro-brain natriuretic peptide as a marker of right ventricular dysfunction in patients with

tetralogy of Fallot after surgical repair. Chest 2005; 128: 2563-2570.

80. Babu-Narayan SV, Kilner PJ, Li W, et al. Ventricular fibrosis suggested by cardiovascular magnetic resonance in adults with repaired tetralogy of Fallot

and its relationship to adverse markers of clinical outcome. Circulation 2006; 113: 405-413.

81. Festa P, Ait-Ali L, Prontera C, et al. Amino-terminal fragment of pro-brain natriuretic hormone identifies functional impairment and right ventricular

overload in operated tetralogy of Fallot patients.　Pediatr Cardiol 2007; 28: 339-345.

82. Ohuchi H, Hisashi T, Ohashi H, et al. Abnormalities of Neurohormonal and Cardiac Autonomic Nervous Activities Relate Poorly to Functional Status in

Fontan Patients. Circulation 2004; 110: 2601-2608.

83. Bolger AP, Sharma R, Li W, et al. Neurohormonal activation and the chronic heart failure syndrome in adults with congenital heart disease. Circulation

2002; 106: 92-99.

84. Giannakoulas G, Dimopoulos K, Bolger AP, et al. Usefulness of natriuretic Peptide levels to predict mortality in adults with congenital heart disease.

Am J Cardiol 2010; 105: 869-873.

85. Szymañski P, Klisiewicz A, Lubiszewska B, et al. Application of classic heart failure definitions of asymptomatic and symptomatic ventricular

dysfunction and heart failure symptoms with preserved ejection fraction to patients with systemic right ventricles. Am J Cardiol 2009; 104: 414-418.

86. Qi W, Mathisen P, Kjekshus J, et al. Natriuretic peptides in patients with aortic stenosis, Am Heart J 2001; 142: 725-732.

87. Gerber IL, Stewart RL, Legget ME, et al. Increased plasma natriuretic peptide levels reflect symptom onset in aortic stenosis, Circulation 2003; 107:

1884-1890.

88. Cheung EW, Lam WW, Chiu CS, et al. Plasma brain natriuretic peptide levels, right ventricular volume overload and exercise capacity in adolescents

after surgical repair of tetralogy of Fallot. Int J Cardiol 2007; 121: 155-162.

89. Chow PC, Cheung EW, Chong CY, et al. Brain natriuretic peptide as a biomarker of systemic right ventricular function in patients with transposition of

great arteries after atrial switch operation. Int J Cardiol 2008; 127: 192-197.

90. Atz AM, Zak V, Breitbart RE, et al. Factors associated with serum brain natriuretic peptide levels after the Fontan procedure. Congenit Heart Dis 2011

Mar 25. doi: 10.1111/j.1747-0803.2011.00496.x. [Epub ahead of print].

91. Fredriksen PM, Veldtman G, Hechter S, et al. Aerobic capacity in adults with various congenital heart diseases. Am J Cardiol 2001; 87: 310-314.

92. Iivainen TE, Groundstroem KW, Lahtela JT, et al. Serum N-terminal atrial natriuretic peptide in adult patients late after surgical repair of atrial septal

defect. Eur J Heart Fail 2000; 2: 161-165.

93. Pillutla P, Shetty KD, Foster E. Mortality associated with adult congenital heart disease: Trends in the US population from 1979 to 2005. Am Heart

J 2009; 158: 874-879.

94. Neumayer U, Stone S, Somerville J, et al. Small ventricular septal defects in adults. Eur Heart J 1998; 19: 1573-1582.

95. Gabriel HM, et al. Long-term outcome of patients with ventricular septal defect considered not to require surgical closure during childhood. J Am Coll

Cardiol 2002; 39: 1066-1071.

96. Hunt SA, Baker DW, Chin MH, et al. ACC/AHA Guidelines for the Evaluation and Management of Chronic Heart Failure in the Adult: Executive

Summary. Circulation 2001; 104: 2996-3007.

97. 藤田修平，高橋一浩，竹内大二，他．成人先天性心疾患における心不全．日本心臓病学会誌 2009；3：216-221.

98. Moller JH, Anderson RC. 1,000 consecutive children with a cardiac malformation with 26- to 37-year follow-up. Am J Cardiol 1992; 70: 661-667.

99. 丹羽公一郎，浜田洋通，中澤誠，他．ファロー四徴症心内修復術後例の長期遠隔期の罹病率とQOL─多施設共同研究報告─．J Cardiol 2001；37 Supple I：

284.

100. Samman A, Schwerzmann M, Balint OH, et al. Exercise capacity and biventricular function in adult patients with repaired tetralogy of Fallot. Am Heart

J 2008; 156: 100-105.

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